Can anyone direct me to clinical patient references or treatment options for a 34 y.o. pregnant client with familial chylomicronemia, an auto-recessive inherited very rare inborn error of metabolism in which no lipoprotein lipase exists to clear fats from the blood. Consequently, even on a very low fat diet, triglycerides build up to extreme levels leading to pancreatitis. 

Client was diagnosed at age 10 after 3 pouts of pancreatitis. She has been on an < 15-30 gram/day fat diet, and avoided all alcohol which has controlled her condition well. She has had about 4 other pancreatitis episodes to date when off this very stringent diet. 

Her first challenge will be a healthy pregnancy due to a steep rise in estrogen which can raise triyglycerides even in "normal"
pregnant women.

Her second will be breastfeeding.  I know she badly wants to breastfeed as her mom is a Lactation Consultant/former La Leche League Leader. She was herself a longterm breastfeeding toddler.  I am her mother.

The only info I have been able to get is that her breastmilk will have an absence of long chain fatty acids.  

Any information will be greatly appreciated.

Laura Monin BA CLE IBCLC, RLC
San Francisco, California

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